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Vulvar Lymphangioma Circumscriptum Secondary to Crohn Disease
Mayo Clinic ProceedingsVol. 96Issue 11p2923–2924Published in issue: November, 2021- Kristin N. Petit
- Danielle M. Petit
- Alina G. Bridges
Cited in Scopus: 0A 56-year-old woman presented to the dermatologist for worsening vulvar papules and edema for 3 years. She had Crohn disease in remission status post colectomy with ileostomy and vaginal fistula repair. Prior nondiagnostic biopsies performed by the gynecology service showed squamous hyperplasia, lichenoid features, acute and chronic inflammation, and dermal fibrosis. The labia were markedly edematous, with clear to hemorrhagic papules and vesicles coalescing to a papillomatous plaque (Figure 1).