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Desmoid Tumor

      Desmoid tumor involving the small bowel.
      Which of the following statements is most accurate regarding desmoid tumors?
      • a.
        Sporadic desmoid tumors occur only in an intraabdominal location
      • b.
        Desmoid tumors are almost universally fatal
      • c.
        Desmoid tumors can occur in familial adenomatous polyposis
      • d.
        Desmoid tumors never show invasion
      Answer: c. Desmoid tumors can occur in familial adenomatous polyposis.
      Desmoid tumors often occur sporadically, but they occur in 10% to 25% of individuals with familial adenomatous polyposis.
      • Campos F.G.
      • Martinez C.A.
      • Novacs M.
      • Nahas S.C.
      • Cecconello I.
      Desmoid tumors: clinical features and outcome of an unpredictable and challenging manifestation of familial adenomatous polyposis.
      Sporadic desmoid tumors can occur in intraabdominal or extraabdominal locations, whereas those associated with familial adenomatous polyposis are most often intraabdominal.
      • Campos F.G.
      • Martinez C.A.
      • Novacs M.
      • Nahas S.C.
      • Cecconello I.
      Desmoid tumors: clinical features and outcome of an unpredictable and challenging manifestation of familial adenomatous polyposis.
      The behavior of desmoid tumors can vary from indolent to aggressive.

      Reference

        • Campos F.G.
        • Martinez C.A.
        • Novacs M.
        • Nahas S.C.
        • Cecconello I.
        Desmoid tumors: clinical features and outcome of an unpredictable and challenging manifestation of familial adenomatous polyposis.
        Fam Cancer. 2015; 14: 211-219